E31.21 Multiple endocrine neoplasia [MEN] type I

Instructional Notes:

E31.21
Description: Multiple endocrine neoplasia [MEN] type I
Inclusion Term:
- Wermer's syndrome
↓
E31.2
Description: Multiple endocrine neoplasia [MEN] syndromes
Inclusion Term:
- Multiple endocrine adenomatosis
Code Also: ['any associated malignancies and other conditions associated with the syndromes']
↓
E31
Description: Polyglandular dysfunction
Exclude1:
- ataxia telangiectasia [Louis-Bar] (G11.3)
- dystrophia myotonica [Steinert] (G71.11)
- pseudohypoparathyroidism (E20.1)
↓
E20-E35
Description: Disorders of other endocrine glands (E20-E35)
Exclude1:
- galactorrhea (N64.3)
- gynecomastia (N62)
↓
E00-E89
Description: Endocrine, nutritional and metabolic diseases
Exclude1:
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Notes:
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.